Acute hemolytic crisis with fulminant hepatic failure as the first manifestation of Wilson's disease: a case report.

نویسندگان

  • J. J. Lee
  • H. J. Kim
  • I. J. Chung
  • H. Kook
  • J. R. Byun
  • S. Y. Kwon
  • M. R. Park
  • K. S. Choi
  • T. J. Hwang
  • D. W. Ryang
چکیده

We report a 27-year-old woman who developed Coombs' negative hemolytic anemia and fulminant hepatic failure as the initial manifestation of Wilson's disease. Unmeasurably low level of serum alkaline phosphatase provided a clue to the diagnosis of Wilson's disease. The diagnosis was established with the presence of Kayser-Fleischer ring, decreased serum ceruloplasmin level, and elevated urine and serum copper levels. In spite of repeated plasmapheresis, she died of multiorgan failure on the fifth hospital day.

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عنوان ژورنال:
  • Journal of Korean Medical Science

دوره 13  شماره 

صفحات  -

تاریخ انتشار 1998